Diurnal variability of glucose tetrasaccharide (Glc 4) excretion in patients with glycogen storage disease type III

Diurnal variability of glucose tetrasaccharide (Glc 4) excretion in patients with glycogen storage disease type III

The urinary glucose tetrasaccharide, Glcα1-6Glcα1-4Glcα1-4Glc (Glc4), is a glycogen restrict dextrin that’s elevated in sufferers with glycogen storage illness (GSD) kind III. We evaluated the potential of raw cornstarch remedy to intervene with Glc4 monitoring, by measuring the diurnal variability of Glc4 excretion in sufferers with GSD III. Voids had been collected at dwelling over 24 […]